Porphyria attacks can be deadly

• April 20, 2024

The porphyrias they are a group of hereditary disorders in which a significant part of the hemoglobin , call heme (is the storage of iron in the Red blood cells , responsible for the transport of oxygen in the body), does not occur properly.

The production of porphyrins causes different symptoms in the nervous system and in the skin . There are many different ways to porphyria and the most common type is Delayed cutaneous porphyria (PCT), which is acquired unlike the others.

This condition may appear during the first years of life, but sometimes appears at puberty or in adulthood. It usually occurs between 20 and 40 years of age.

This disease affects mainly the women, whose attacks are related to the menstrual cycle . They can be distant from each other and can be triggered by the consumption of alcohol, drugs , subsistence allowance and the infections .

The porphyrias They involve three main symptoms:

1. Colic or abdominal pain (only in some forms of the disease) 2. Sensitivity to light that causes rashes, blisters and scarring of the skin (photodermatitis ) 3. Problems with the nervous and muscular systems (seizures , mental alterations, damage neurological )

So that you know a little more about these disorders, in GetQoralHealth we present the testimony of patients who suffer from it:

The porphyria attacks can occur suddenly, usually with stomach ache strong, followed by threw up Y constipation . They can even become mortal.

During a acute attack , the balance of electrolytes , the blood , they administer carbohydrates , administration of painkillers and / or sedatives .

For the chronic treatment of the disease, it is recommended not to consume alcohol , avoid medication that precipitates attacks , a diet rich in carbohydrates , avoid exposure to sunlight , employment of sunscreen , consume beta carotene , avoid cutaneous traumas .

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Video Medicine: Story of a Patient Living with Variegate Porphyria (April 2024).